Date | 2016.03 | 2020.07 | 2023.03 |
---|---|---|---|
Age | 25 | 30 | 32 |
Right heart catheterization | Â | Â | Â |
 PAP (S/D/M, mmHg) | 65/29/43 | 87/29/50 | – |
 PAWP (mmHg) | 8 | 8 | – |
 RAP (mmHg) | 10 | 10 | – |
 CI (L/min/m2) | 2.08 | 2.16 | – |
 PVR (Wood Units) | 12.5 | 14.29 | – |
 SVR (Wood Units) | 27.38 | 23.8 | – |
 SaO2 (%) | 94 | 93 | – |
Echocardiogram | Â | Â | Â |
 LVEDd (mm) | 38 | 39 | 36 |
 LVEF (%) | 59 | 50 | 52 |
 RVd (mm) | 35 | 41 | 42 |
 PA (mm) | 32 | 32 | 33 |
 Peak TRV (m/s) | 3.2 | 2.8 | 3.1 |
 TAPSE (mm) | – | 12 | 15 |
 RV-FAC (%) | – | 26 | 29 |
 IVC (mm) | 12 | 15 | 13 |
 Pericardial effusion | No | Minimal | No |
 NT-proBNP (pg/ml) | 628 | 3020 | 352 |
 6MWD (m) | 496 | 294 | 482 |
 WHO-FC | II | III | II |
 Medication | Silenafil, Bosentan | Sildenafil, Macitentan, Treprostinil | Sildenafil, Macitentan, Selexipag |