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Table 2 Clinical parameters reflecting differences between non-sCSD and sCSD patients

From: Isolated choanal and gut atresias: pathogenetic role of serine protease inhibitor type 2 (SPINT2) gene mutations unlikely

Parameter

non-sCSD

sCSD

p value

Actual age (months)

139 ± 101

60 ± 70

< 0.05

Gestational age (weeks)

39 ± 2

37 ± 3

< 0.05

Birth weight (g)

3136 ± 554

2900 ± 448

n.s.

Plasma Na (mmol/L)

140 ± 2

120 ± 4

< 0.001

Plasma pH

7.34 ± 0.07

7.18 ± 0.11

< 0.001

Urinary Na (mmol/L)

139 ± 64

10 ± 4

< 0.001

FENa (%)

1.2 ± 0.7

0.1 ± 0.0

< 0.001

uNa/uCrea (mmol/mmol)

25.0 ± 11.1

0.9 ± 0.4

< 0.001

Fecal Na (mmol/L)

29 ± 9

106 ± 33.2

< 0.001

Fecal pH

6.5 ± 1.1

7.3 ± 1.1

n.s.

  1. Abbreviations in alphabetical order: FE Na fractional excretion of sodium; mo month; n.s. not significant; uNa/uCrea urinary Na/urinary creatinine ratio; wk week