Table 1 General Information and dominant clinical features in patients
Patient | Age at CPSS diagnosis/ gender | Type of CPSS | Associated cardiac conditions | Other combined diseases | Clinical manifestation | Have PAH or not |
|---|---|---|---|---|---|---|
1 | 19/F | CEPS: type I | PDA1.5 mm | Straight back syndrome | Cough, palpitation | YES |
2 | 18/M | CEPS: type II | None | None | Palpitation, shortness of breath, syncope | YES |
3 | 10/M | CEPS: type II | ASD13mm | Polymyositis (PM)/Dermatomyositis (DM) | Physical decline, shortness of breath | YES |
4 | 20/F | CIPS | ASD16 + 9 mm | Hepatic hemangioma | Cyanosis, syncope | YES |
5 | 4/M | CEPS: type II | None | Thrombocytopenia | Physical decline, dyspnea, chest discomfort | YES |
6 | 31/F | CIPS | None | Mixed connective tissue disease (MCTD), Iron-deficiency anemia (IDA) | Physical decline | NO |