Table 1 Summary of cases of congenital absence of the portal vein (CAPV) with focal nodular hyperplasia (FNH)
Case | Author | Year | Age (y) | Sex | Type | Hepatic Tumor | Other anomalies | Other disorders |
|---|---|---|---|---|---|---|---|---|
1 | Morse [33] | 1986 | 8 | F | Ia | FNH (Solitary) | ASD, Goldenhar syndrome | LD |
2 | Matsuoka [34] | 1992 | 22 | F | Ib | FNH (Solitary) | Scoliosis with hemivertebra | LD |
3 | Motoori [39] | 1997 | 18 | F | Ib | FNH (Multiple) | Pancreatic tumor | LD |
4 | Guariso [32] | 1998 | 8 | F | Ib | FNH (Solitary) | Cystic kidney dysplasia | None |
5 | Wakamoto [31] | 1999 | 6 | F | Ib | FNH (Solitary) | PDA, Inguinal herniation | LD, Hyperammonemia |
6 | Kinjio [38] | 2001 | 3 | F | Ib | FNH (Multiple) | Congenital choledochal cyst | LD, Encephalopathy |
7 | Tanaka [37] | 2003 | 16 | F | Ib | FNH (Multiple) | Chronic active hepatitis | LD |
8 | De Gaetano [5] | 2004 | 28 | F | Ib | FNH (Multiple) | None | None |
9 | Schmidt [36] | 2006 | 18 | F | Ib | FNH (Multiple) | None | LD |
10 | Turkbey [4] | 2006 | 10 | F | Ia | FNH (Multiple) | None | LD |
11 | Morotti [41] | 2007 | 8 | F | Ia | FNH, HCC, adenoma | TS, Aortic coarctation | LD |
12 | Ringe [35] | 2008 | 12 | M | Ib | FNH (Multiple) | None | LD, Encephalopathy |
13 | Ringe [35] | 2008 | 22 | M | Ib | FNH (Multiple) | None | LD, Encephalopathy |
14 | Chandler [40] | 2011 | 24 | M | Ib | FNH (Multiple) | None | LD |