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Table 1 Summary of cases of congenital absence of the portal vein (CAPV) with focal nodular hyperplasia (FNH)

From: Computed tomography and magnetic resonance imaging of multiple focal nodular hyperplasias of the liver with congenital absence of the portal vein in a Chinese girl: case report and review of the literature

Case Author Year Age (y) Sex Type Hepatic Tumor Other anomalies Other disorders
1 Morse [33] 1986 8 F Ia FNH (Solitary) ASD, Goldenhar syndrome LD
2 Matsuoka [34] 1992 22 F Ib FNH (Solitary) Scoliosis with hemivertebra LD
3 Motoori [39] 1997 18 F Ib FNH (Multiple) Pancreatic tumor LD
4 Guariso [32] 1998 8 F Ib FNH (Solitary) Cystic kidney dysplasia None
5 Wakamoto [31] 1999 6 F Ib FNH (Solitary) PDA, Inguinal herniation LD, Hyperammonemia
6 Kinjio [38] 2001 3 F Ib FNH (Multiple) Congenital choledochal cyst LD, Encephalopathy
7 Tanaka [37] 2003 16 F Ib FNH (Multiple) Chronic active hepatitis LD
8 De Gaetano [5] 2004 28 F Ib FNH (Multiple) None None
9 Schmidt [36] 2006 18 F Ib FNH (Multiple) None LD
10 Turkbey [4] 2006 10 F Ia FNH (Multiple) None LD
11 Morotti [41] 2007 8 F Ia FNH, HCC, adenoma TS, Aortic coarctation LD
12 Ringe [35] 2008 12 M Ib FNH (Multiple) None LD, Encephalopathy
13 Ringe [35] 2008 22 M Ib FNH (Multiple) None LD, Encephalopathy
14 Chandler [40] 2011 24 M Ib FNH (Multiple) None LD
  1. ASD, atrioventricular septal defect; CAPV, congenital absence of the portal vein; FNH, focal nodular hyperplasia; HCC, hepatocellular carcinoma; LD, liver dysfunction; PDA, patent ductus arteriosus; TS, Turner syndrome.