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Table 3 Hearing assessments of MEM subtypes

From: ENT characteristics and therapeutic results in multisystemic disorders of mitochondrial encephalomyopathy

MEM subtypes

PTA N

PTA Ab

AI

DPOAE N

ABR N

SDS N

AI

DPOAE Ab (N%)

ABR Ab (N%)

SDS Ab (N%)

T N

ASR N

T Ab

ASR Ab

CPEO

7(21.9)

7(21.9)

6(18.8)

6(18.8)

7(21.9)

0(0)

7(21.9)

8(25)

8(25)

3(9.4)

MELAS

2(6.3)

2(6.3)

1(3.1)

1(3.1)

2(6.3)

0(0)

3(9.4)

3(9.4)

3(9.4)

2(6.3)

KSS

1(3.1)

1(3.1)

1(3.1)

1(3.1)

1(3.1)

0(0)

4(12.5)

4(12.5)

4(12.5)

2(6.3)

MIDD

0(0)

0(0)

0(0)

0(0)

0(0)

0(0)

4(12.5)

4(12.5)

4(12.5)

0(0)

LION

3(9.4)

3(9.4)

3(9.4)

3(9.4)

3(9.4)

0(0)

0(0)

0(0)

0(0)

0(0)

  1. N normal, Ab abnormal, PTA pure tone average, AI acoustic immittance, T tympanogram, ASR acoustic stapediusreflex, DPOAE distortion product otoacoustic emissions, ABR auditory brainstem response, SDS speech discriminationscore